Modern approaches to the treatment of congenital neutropenia

نویسندگان

چکیده

Neutropenia is common in the practice of both primary care physicians and sub-speciality. Congenital neutropenia are rare diseases; they can be isolated independent diseases accompany a number other inborn errors immunity. The clinical course range from asymptomatic patients with mild to life-threatening infections cases severe neutropenia. Treatment congenital remains discutable this day. most accessible method treatment granulocyte colony-stimulating factor, although it does not cure disease prevent development malignant transformation. On hand, use factor correct doses improve disease, quality life patients, avoid septic complications. Hematopoietic stem cell transplant an effective for that respond therapy. Modern methods genetic therapy open new perspectives No conflict interests was declared by author. Key words: neutropenia, treatment, Granulocyte (G-CSF).

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ژورنال

عنوان ژورنال: Su?asna pedìatrìâ. Ukraïna

سال: 2022

ISSN: ['2706-6134', '2663-7553']

DOI: https://doi.org/10.15574/sp.2022.123.80